PIBI(D)S syndrome is similar to BIDS syndrome, but also associated with photosensitivity, and in contrast to IBIDS syndrome, the ichthyosis is mild and not congential.[1]:501 Additionally, there is a relationship with xeroderma pigmentosum in that virtually all PIBI(D)S patients have a deficiency in the nucleotide excision repair of UV-induced DNA damage that is indistinguishable from that of xeroderma pigmentosum group D.[1]:501